Lymphangiomatosis: a differential diagnosis of lytic lesions of the temporal bone.

Lymphangiomatosis: a differential diagnosis of lytic lesions of the temporal bone.
J Laryngol Otol. 2008 Jul
Naguib MB, Al-Jazan N, Hashem T.
Department of Otolaryngology, King Faisal University, Al-Khobar, Saudi Arabia.

Objective: We report a histologically proved case of lymphangiomatosis of the skull, involving the temporal bone and presenting as multiple lytic bone lesions.Method:A case report and a review of the literature concerning lymphangiomatosis are presented.

Results: Lymphangiomatosis affecting bones is a rare disorder caused by a congenital malformation of the lymphatic system, resulting in diffuse proliferation of the lymphatic channels and involving bones, parenchymal organs and soft tissue. Involved bones show massive osteolysis and progressive, localised bone resorption.

Conclusion: Lymphangiomatosis should be kept in mind in the differential diagnosis of lytic lesions of the skull.

PMID: 18667106 [PubMed - as supplied by publisher]