Developmental Disorders of the Lymphatics

An information blog for disorders of the lymphatics. For all articles, please click on "Archives" - Due to spammers, I will no longer allow comments, sorry.

Saturday, January 12, 2013

Bilateral renal lymphangiomatosis: imaging and histopathologic findings.

Bilateral renal lymphangiomatosis: imaging and histopathologic findings.

Jan 2013


Service d'Anatomie et de Cytologie Pathologiques, Université Paris-Sud 11, APHP, Hôpital de Bicêtre, CHU de Bicêtre, 78 rue du Général Leclerc, 94275, Le Kremlin-Bicêtre, France,


Renal lymphangiomatosis is an extremely rare disease characterized by developmental malformation of the lymphatic system surrounding the kidneys. We present the case of a 22-year-old pregnant female discovered because of worsening. Ultrasound, computed tomography, and magnetic resonance imaging studies were performed. An 18 × 11 × 10 cm voluminous cystic subcapsular lesion compressing the left kidney and subcapsular cysts of the right kidney were found. After the delivery, marsupialization was performed and the pathological analysis confirmed the diagnosis of lymphangiomatosis. A review of the literature is proposed.

Labels: , , , ,