Congenital Lymphangioma Circumscriptum of the Vulva.

Congenital Lymphangioma Circumscriptum of the Vulva

Indian Pediatr. 2009 May

Aggarwal K, Gupta S, Jain VK, Marwah N.
Department of Dermatology, Venereology and Leprology and Department of Pathology, Post Graduate Institute of Medical Sciences and Research, Rohtak, India; and Department of Dermatology, Venereology and Leprology, MM Institute of Medical Sciences and Research, Mullana, Ambala, India. Correspondence to: Dr Sanjeev Gupta, HNo B2, Near Shiv Mandir, MM Medical College Residential Campus, Mullana, District Ambala, Haryana 133 203. India. sanjeevguptadr@yahoo.com.

Lymphangioma circumscriptum of the vulva is a disorder of lymphatic channels involving deep dermal tissues. Most of these cases are confused with genital warts leading to improper diagnosis and treatment. We present a three years young female child who had multiple skin colored papular lesions over the genitals. Skin biopsy revealed features of lymphangioma circumscriptum.

IndianPediatrics.net (Full Text Article PDF)

Radiotherapy in congenital vulvar lymphangioma circumscriptum.

Radiotherapy in congenital vulvar lymphangioma circumscriptum.

Int J Gynecol Cancer. 2007 Aug

Yildiz F, Atahan IL, Ozyar E, Karcaaltincaba M, Cengiz M, Ozyigit G, Aydin A, Usubütün A, Ayhan A.

Ferah Yildiz, MD, Department of Radiation Oncology, Faculty of Medicine, Hacettepe University, 06100 Ankara, Turkey. Email: fyildiz@hacettepe.edu.tr

Department of Radiation Oncology, Faculty of Medicine, Hacettepe University, Ankara, Turkey.

Congenital lymphangioma circumscriptum (LC) of the vulva is a rare disorder with unknown etiology. Treatment options include ablative approaches such as laser therapy, sclerotherapy, and surgery. Radiotherapy has been shown to be effective in the management of congenital lymphangioma especially in the thoracic and abdominal lesions. In this report, we describe a patient with persistent vulvar LC despite sclerosing therapy and several surgical excisions. She was treated with a course of external radiotherapy and showed a dramatic objective response with relief of all symptoms.

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