Developmental Disorders of the Lymphatics

An information blog for disorders of the lymphatics. For all articles, please click on "Archives" - Due to spammers, I will no longer allow comments, sorry.

Monday, June 08, 2009

Abdominal lymphangioma in children: Report of three cases.

Abdominal lymphangioma in children: Report of three cases.
Surg Today. 2009
Muramori K, Zaizen Y, Noguchi S.
Department of Pediatric Surgery, Matsuyama Red Cross Hospital, Matsuyama, Japan.


Most cases of abdominal lymphangioma are asymptomatic. However, patients may occasionally present with acute abdomen because of an intestinal obstruction or peritonitis caused by infected cysts, hemorrhaging, and/or torsion. These conditions may differ based on the location of the lymphangioma and do not always require emergency surgery. This report presents two cases of abdominal lymphangioma derived from the omentum, which required emergency surgery because of severe abdominal distension and peritonitis caused by torsion, respectively. In contrast, another case of retroperitoneal lymphangioma presented with acute abdomen and underwent elective surgery after conservative therapy for peritonitis. Elective surgery is acceptable if the symptoms are controllable under conservative therapy. However, it is important not to overlook the possible lethal complications such as intestinal and/or urological obstruction, aggressive peritonitis, and torsion of the cyst, which require emergency surgery.

SpringerLink

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Cystic lymphangiomatous hamartoma masquerading as massive ascites.

Cystic lymphangiomatous hamartoma masquerading as massive ascites.
Indian J Pediatr. 2009 May

Parakh A, Dubey AP, Garg A, Khurana N, Aggarwal SK.
Department of Pediatric, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India,
ankitparakh102@rediffmail.com.

We report a 4-year-old boy presenting with a tense massive ascites and large hydrocele. History and physical examination were unremarkable. Routine laboratory studies were normal. Abdominal ultrasonography revealed massive ascites. Contrast CT was suggestive of a large cyst covering the entire peritoneal cavity. At laparotomy, a large cystic tumor was found extending into the scrotum through the left inguinal ring. Histopathologic examination diagnosed the tumor as a cystic lymphangiomatous hemartoma. Although abdominal lymphangiomas are seen in children, but presenting as massive ascites with hydrocele is very rare.

SpringerLink

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Congenital Lymphangioma Circumscriptum of the Vulva.

Congenital Lymphangioma Circumscriptum of the Vulva

Indian Pediatr. 2009 May

Aggarwal K, Gupta S, Jain VK, Marwah N.
Department of Dermatology, Venereology and Leprology and Department of Pathology, Post Graduate Institute of Medical Sciences and Research, Rohtak, India; and Department of Dermatology, Venereology and Leprology, MM Institute of Medical Sciences and Research, Mullana, Ambala, India. Correspondence to: Dr Sanjeev Gupta, HNo B2, Near Shiv Mandir, MM Medical College Residential Campus, Mullana, District Ambala, Haryana 133 203. India.
sanjeevguptadr@yahoo.com.

Lymphangioma circumscriptum of the vulva is a disorder of lymphatic channels involving deep dermal tissues. Most of these cases are confused with genital warts leading to improper diagnosis and treatment. We present a three years young female child who had multiple skin colored papular lesions over the genitals. Skin biopsy revealed features of lymphangioma circumscriptum.

IndianPediatrics.net (Full Text Article PDF)

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